PRIMARY OBJECTIVE:
I. To evaluate the safety and tolerability and determine the dose-limiting toxicity and
the maximum tolerated dose (MTD) of the combination of daunorubicin & cytarabine
chemotherapy plus Venetoclax for patients with AML
SECONDARY OBJECTIVES:
I. To assess efficacy by response per 2022 ELN and revised International Working Group
(IWG) criteria.
II. To determine additional response parameters: CR/CRi and CR/CRh rates.
III. To determine time to response variables including overall survival (OS), event-free
survival (EFS) and duration of response (DOR)
EXPLORATORY OBJECTIVES:
I. To assess rates of LSC eradication by means of MFC and single cell sequencing, as well
as a novel assay that uses an extended leukemia-specific NGS panel for measuring MRD in
cfDNA and BM ("high resolution MRD assay")
II. To comprehensively analyze the clonal architectural and transcriptomic shifts in
residual LSC under therapy
III. To determine the protein expression of BCL-2 family members and the reliance of
leukemic cells on differing members of the BH3 family at the time of diagnosis and
relapse and explore association of such observations with response to Venetoclax when
combined with chemotherapy
Dose Escalation Cohorts:
A minimum of 3 patients will be treated in each cohort (dose level) sequentially in a 3+3
design. Patients will receive the Venetoclax plus daunorubicin/cytarabine combination as
shown below
Patients aged ≤ 60 years
Cohort 1A:
Daunorubicin 60mg/m2 intravenously (IV) daily on days 2-4; Cytarabine 100mg/m2 IV daily
on Days 2-8; Venetoclax 100mg orally on Day 1, 200mg on Day 2, 400mg on Days 3-8
Cohort 2A:
Daunorubicin 90mg/m2 IV daily on Days 2-4; Cytarabine 100mg/m2 IV daily on Days 2-8;
Venetoclax 100mg orally on Day 1, 200mg on Day 2, 400mg on Days 3-8
Cohort 3A:
Daunorubicin 60mg/m2 IV daily on Days 2-4; Cytarabine 100mg/m2 IV daily on Days 2-8;
Venetoclax 100mg orally on Day 1, 200mg on Day 2, 400mg on Days 3-11
Cohort 4A:
Daunorubicin 60mg/m2 IV daily on Days 2-4; Cytarabine 100mg/m2 IV daily on Days 2-8;
Venetoclax 100mg orally on Day 1, 200mg on Day 2, 400mg on Days 3-14
Note: No DLTs in induction phase have been observed and Cohort 3A has completed
enrollment. However, the daunorubicin dose of 90mg/m2 will not be further studied due to
recently reported results of no superiority over the dose of 60mg/m2.
Patients >60 years
Cohort 1B:
Daunorubicin 60mg/m2 IV daily on Days 2-4; Cytarabine 100mg/m2 IV daily on Days 2-8;
Venetoclax 100mg orally on Day 1, 200mg on Day 2, 400mg on Days 3-8
Cohort 2B:
Daunorubicin 60mg/m2 IV daily on Days 2-4; Cytarabine 100mg/m2 IV daily on Days 2-8;
Venetoclax 100mg orally on Day 1, 200mg on Day 2, 400mg on Day 3-11
Cohort 3B:
Daunorubicin 60mg/m2 IV daily on Days 2-4; Cytarabine 100mg/m2 IV daily on Days 2-8;
Venetoclax 100mg orally on Day 1, 200mg on Day 2, 400mg on Days 3-14
Expansion Cohort(s):
A maximum of 28 additional patients aged ≤ 60 years and 28 patients >60 years will be
randomized (1:1) to the MTD the starting dose (assuming the MTD is not the starting
dose), to further evaluate safety and efficacy of the study drug combination and identify
the optimal phase 2 dose.
Consolidation Phase:
Patients who achieve CRc post induction will proceed to consolidation therapy with
high-dose cytarabine in combination with escalating doses of Venetoclax. The 3+3
algorithm will be applied for dose escalation/de-escalation of Venetoclax in combination
with Cytarabine. As of February 2023, there have been 2/6 hematologic DLTs in
consolidation cohort 1B, therefore we will no longer give Venetoclax in combination with
high-dose cytarabine during the consolidation phase, in pts >60 yrs of age. We will also
not explore dose escalation of Venetoclax during consolidation in the 60-year-old or
younger age-group before RP2D of induction is determined. All subjects ≤ 60yrs will be
treated at the consolidation Cohort 1A dose.
In the expansion phase, Venetoclax, at the dose of 200mg daily, will be re-introduced in
combination with chemotherapy, albeit at a shorter than a 7-day duration; the
consolidation regimen for patients older than 60 years of age will consist of cytarabine
at the dose of 0.5-1g/m2 every 12 hours on days 1,3,5 or days 1,2,3 (per ELN 2022
guidelines) plus Venetoclax 200mg for 5 days.
Patients ≤ 60 years
Consolidation cohort 1A:
Cytarabine 1.5g/m2 every 12 hours on Days 1, 3, 5 OR days 1, 2, 3; Venetoclax 200mg on
Days 1-7
Patients >60 years
Consolidation cohort 1B:
Cytarabine 0.5-1g/m2 every 12 hours on days 1, 3, 5 OR days 1, 2, 3; Venetoclax 200mg on
Days 1-5
A minimum of 3 patients will be treated in each cohort (dose level) sequentially in a 3+3
design. Additional 3 subjects may be backfilled to lower dose levels so that each cohort
will reach a total of 6 subjects. Once the MTD is reached, a maximum of 28 additional
patients will be randomized 1:1 to the MTD or a dose level below the MTD the starting
dose (assuming the MTD is not the starting dose) for a total of up to 20 patients (6 from
Part 1, 20 from Part 2) treated at each of those dose levels. A maximum of 52 patients
(including backfill and expansion cohorts) 60 years or younger and 46 patients older than
60 years may be enrolled in this Phase 1b study.
Patients will receive one cycle of induction chemotherapy as described above. An interim
bone marrow evaluation will be performed between days 14-21 from chemotherapy initiation.
Patients who will not achieve marrow hypoplasia (cellularity <20% of which less than 5%
are residual blasts) will receive a second induction, as allowed by their clinical
circumstances. Second induction chemotherapy will be comprised of daunorubicin 60mg/m2 x
2 days (45mg/m2 x 2 days in patients initially treated with daunorubicin 90mg/m2) and
cytarabine 100mg/m2 x 5 days along with Venetoclax 400mg for 7 days, whether younger or
older than 60 years of age, and disease assessment will be performed on day 28 (up to day
42) of second induction. Patients who do not achieve CR/CRi after a second induction will
be taken off protocol and will be treated per treating physician's discretion. Patients
who achieve CRc will proceed to consolidation therapy with high-dose cytarabine in
combination with escalating doses of Venetoclax (200-400mg) for up to four 28(-42)-day
cycles, as described above (complete dose adjustment guidelines are outlined in the study
protocol); consolidation with allogeneic transplantation off protocol is allowed per
physician's discretion. The 3+3 algorithm will be applied for dose
escalation/de-escalation of Venetoclax in combination with high-dose cytarabine. Each
cycle of cytarabine will last up to 42 days.
All participants should undergo response evaluations between Day 28 and Day 42 of first
and/or second induction course. Unless there is clear evidence of progressive disease in
the blood, bone marrow aspiration is required and bone marrow biopsy is strongly
encouraged. In cases with hypocellular marrows (<10% cellularity), repeat bone marrow
examinations should be considered when there is evidence of hematopoietic recovery. If
multiple bone marrow examinations are performed, the last examination will be used to
classify the patient's response. The final response will be determined no later than day
42 from the start of therapy.