Phase
Condition
Primary Biliary Cholangitis
Treatment
N/AClinical Study ID
Ages < 4 All Genders
Study Summary
Eligibility Criteria
Inclusion
Inclusion Criteria:
Greater than 14 days old.
Have PN-associated cholestasis defined as at least 2 consecutive direct bilirubin >2mg/dL with anatomical or functional short gut (OR >4 mg/dL if intact intestine)obtained at least 1 week apart with a ratio of direct: total bilirubin > 0.4.
Patients will be PN dependent (unable to meet nutritional needs solely by enteralnutrition) and are expected to require PN for at least 4 more weeks.
Patients must have failed standard therapies for Parenteral Nutrition Associated LiverDisease (PNALD) including: cycling of PN, avoiding overfeeding, reduction/removal ofcopper and manganese from PN, advancement of enteral feeding, and use of ursodiol (i.e. Actigall).
Signed patient informed consent.
The patient is expected to have a reasonable possibility of survival.
No other known etiology of cholestasis other than PNALD at time of Omegaven®initiation.
Exclusion
Exclusion Criteria:
Causes of cholestasis other than PNALD including but not limited to Hepatitis C,Cystic fibrosis, biliary atresia, and alpha 1 anti-trypsin deficiency, prior toOmegaven® initiation.
Known fish or egg allergy
Any of the contraindications to use of Omegaven®:
Active new infection at the time of initiation of Omegaven®
Hemodynamic instability
Use of medications with associated risk of bleeding, including nonsteroidalantiinflammatory drugs (NSAIDs)
Active coagulopathy or bleeding
Thrombocytopenia
Unstable hyperglycemia
Impaired lipid metabolism (triglycerides >1000 mg/dL) while on 1 g/kg/day or lessof Intralipid
History of severe hemorrhagic disorders (ie. hemophilia, Von Willebrand disease,etc.)
Unstable diabetes mellitus
Collapse and shock
Stroke/ Embolism
Cardiac infarction within the last 3 months
Undefined coma status
Enrollment in a clinical trial involving an investigational agent (unless approved bythe designated physicians on the multidisciplinary team)
The parent or guardian of child is unwilling to provide consent or assent
Study Design
Connect with a study center
Carle Foundation Hospital
Urbana, Illinois 61801
United StatesActive - Recruiting
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